a Unidad Médico-Quirúrgica de Enfermedades Respiratorias. Área de Neumopatías Intersticiales y Ocupacionales. Hospital Universitario Virgen del Rocío. OSSES A, RODRIGO; GONZALEZ B, SERGIO; AGUIRRE Z, MARCIA SALDIAS P, FERNANDO. Histiocitosis de células de Langerhans pulmonar: Caso clínico. La histiocitosis de células de Langerhans es una enfermedad . Tras plantearse el caso como histiocitosis hepático y/o pulmonar).4 Su presentación.

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Langerhans cell histiocytosis – Wikipedia

Recurrent cytogenetic or genomic hiztiocitosis would also be required to demonstrate convincingly that LCH is a malignancy. September Pages After six months of follow up, the patient is in good conditions. Der Hautarzt in German. CS1 German-language sources de Infobox medical condition new All articles with unsourced statements Articles with unsourced statements from April Commons category link is locally defined.

A high resolution chest CT scan showed histiociitosis cystic structures predominating in the upper lobes, with small centrilobular nodules.

Relapsing nodular lesions in the course of adult pulmonary Langerhans cell histiocytosis. Initially routine blood tests e.

Radiology will show osteolytic bone lesions and damage to the lung. This page was last uistiocitosis on 1 Decemberat Endocrine deficiency often require lifelong supplement e. Archivos de Bronconeumologia http: Local steroid cream is applied to skin lesions.


Solitary bone lesion may be amenable through excision or limited radiation, dosage of Gy for children, Gy for adults.

Determinants of survival in pulmonary Langerhans’ cell granulomatosis histiocytosis X. Int J Clin Exp Pathol. The Impact Factor pulmonarr the average number of citations received in a particular year by papers published in the journal during the two receding years.

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Murphy tried to diagnose Langerhans cell histiocytosis in a boy with a previously diagnosed osteosarcoma. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact.

New England Journal pulmonad Medicine. Print Send to a friend Export reference Mendeley Statistics.

LCH usually bistiocitosis children between 1 and 15 years old, with a peak incidence between 5 and 10 years of age. Histiocytic sarcoma Langerhans cell sarcoma Interdigitating dendritic cell sarcoma Follicular dendritic cell sarcoma.

It typically has no extraskeletal involvement, but rarely an identical lesion can be found in the skin, lungs, or stomach. Peak onset is 2—10 years of age. Diagnosis is confirmed histologically by tissue biopsy. Assessment of endocrine function and bonemarrow biopsy are also performed when indicated. Journal of Clinical Pathology. A transbronchial biopsy showed a lymphocytic lung infiltrate with Langerhans cells. Open biopsy for chronic diffuse infiltration lung disease: Other types of articles such as reviews, editorials, special articles, clinical reports, and letters to the Editor are also published in the Journal.


Clinical outcomes of pulmonary Langerhans’- cell histiocytosis in adults. LCH provokes a non-specific inflammatory responsewhich includes fever, lethargyand weight loss. British Journal of Dermatology. Langerhans cell histiocytosis Micrograph showing a Langerhans cell histiocytosis with the characteristic reniform Langerhans cells accompanied by abundant eosinophils.

There are ongoing investigations to determine whether LCH is a reactive non-cancerous or neoplastic cancerous process. Unifocal LCH, also called eosinophilic granuloma an older term which is now known to be a misnomeris a slowly progressing disease characterized by an expanding proliferation of Langerhans cells in various bones.

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